
Isovaleric acid - Wikipedia
Isovaleric acid, also known as 3-methylbutanoic acid or β-methylbutyric acid, is a branched-chain alkyl carboxylic acid with the chemical formula (CH 3) 2 CHCH 2 CO 2 H. It is classified as a …
Isovaleric acid | C5H10O2 | CID 10430 - PubChem
Isovaleric acid is a C5, branched-chain saturated fatty acid. It has a role as a plant metabolite and a mammalian metabolite. It is a short-chain fatty acid, a methylbutyric acid and a branched …
Isovaleric acidemia - Wikipedia
Isovaleric acidemia is a rare autosomal recessive [2] metabolic disorder which disrupts or prevents normal metabolism of the branched-chain amino acid leucine. It is a classical type of …
Isovaleric Acid - an overview | ScienceDirect Topics
Isovaleric acid is a branched chain aliphatic saturated carboxylic acid, which can be rapidly absorbed from the gastrointestinal tract and metabolized to innocuous products in the body.
Isovaleric acidemia: Symptoms, causes, treatments, and more
Jan 25, 2024 · Isovaleric acidemia (IVA) is a rare condition that children can inherit from both their biological parents. It can cause serious problems with how the body breaks down proteins. IVA …
Isovaleric acid 99 503-74-2 - MilliporeSigma
Isovaleric acid, also known as 3-methylbutanoic acid, is commonly used for ester synthesis and as a building block in organic reactions. It is a volatile organic compound present in vinegar …
Classic Isovaleric Acidemia - GeneReviews® - NCBI Bookshelf
Mar 14, 2024 · When classic isovaleric acidemia (IVA) is suspected during the diagnostic evaluation, that is, because of increased C5-carnitine concentrations in dried blood spots …
Butanoic acid, 3-methyl- - NIST Chemistry WebBook
Other names: Isovaleric acid; β-Methylbutyric acid; Acetic acid, isopropyl-; Delphinic acid; Isopentanoic acid; Isopropylacetic acid; 3-Methylbutanoic acid; 3-Methylbutyric acid; iso …
Isovaleric Acid - Milk The Funk Wiki
Dec 23, 2023 · Isovaleric Acid, also known as 3-Methylbutanoic acid, is an organic compound with the formula (CH3)2CHCH2CO2H. The flavor and aroma are often described as "pungent …
Isovaleric acidemia: Therapeutic response to supplementation …
Isovaleric acidemia (IVA; MIM 243500) is an autosomal recessive disorder of organic acid metabolism caused by a deficiency of isovaleryl-CoA dehydrogenase (IVD). IVD catalyzes the …
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